Mastoid abscess as a presenting complaint of  Kostmann syndrome in childhood
Kostmann disease is a rare born-with disorder seen as extreme neutropenia due to abnormally low myeloid differentiation in the bone marrow, with the neutrophil count being less than 500_103 cells/l. Male child 4.5-year old complains from a bilateral aural discharge of 2 years duration. By examination, there is a gapped post auricular wound with necrosis in parts and inflamed lower ... Read more